arrhythmogenic right ventricular cardiomyopathy
Also written as: ARVC — Arrhythmogenic Right Ventricular Cardiomyopathy
A hereditary cardiomyopathy characterized by fibrofatty replacement of right ventricular myocardium, predisposing to ventricular arrhythmias.
Full Definition
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiomyopathy characterized by progressive fibrofatty replacement of the right ventricular myocardium. This structural abnormality creates a substrate for ventricular arrhythmias, particularly in young athletes. The condition is associated with sudden cardiac death and requires careful evaluation with imaging, genetic testing, and electrophysiologic assessment. Treatment often involves activity restriction, antiarrhythmic medications, and implantable cardioverter-defibrillator placement.
Usage
Usage note: Often abbreviated as ARVC; previously known as ARVD (arrhythmogenic right ventricular dysplasia).
In Context
- "The patient's family history of sudden cardiac death and epsilon waves on ECG raised suspicion for arrhythmogenic right ventricular cardiomyopathy." — Clinical case report
- "Cardiac MRI revealed right ventricular wall motion abnormalities consistent with ARVC." — Imaging study interpretation