Aortopulmonary Window
Rare congenital heart defect characterized by an abnormal communication between the ascending aorta and pulmonary artery.
Full Definition
An aortopulmonary window is a rare congenital cardiac anomaly consisting of a defect in the septum between the ascending aorta and main pulmonary artery, creating abnormal communication between these great vessels. This condition results in left-to-right shunting with eventual development of pulmonary hypertension and Eisenmenger syndrome if left untreated. The defect is classified by location: proximal (type I), distal (type II), or total septal defect (type III). Surgical repair is typically performed in infancy and involves patch closure of the defect, often requiring cardiopulmonary bypass. Early diagnosis and intervention are crucial to prevent irreversible pulmonary vascular disease.
Usage
Usage note: Often abbreviated as AP window; specify the anatomic type when known.
In Context
- "The infant was diagnosed with a large aortopulmonary window requiring urgent surgical repair to prevent development of pulmonary hypertension." — Pediatric cardiology consultation
- "Echocardiography and cardiac catheterization confirmed a type II aortopulmonary window with significant left-to-right shunting." — Diagnostic report