restrictive cardiomyopathy
Also written as: RCM — restrictive cardiomyopathy
Cardiomyopathy characterized by impaired ventricular filling due to increased myocardial stiffness with preserved systolic function.
Full Definition
Restrictive cardiomyopathy is the least common form of cardiomyopathy, characterized by abnormal diastolic function with impaired ventricular filling due to increased myocardial stiffness. Unlike other cardiomyopathies, systolic function is typically preserved. The condition can be idiopathic or secondary to infiltrative diseases such as amyloidosis, sarcoidosis, or hemochromatosis. Pathological features include interstitial fibrosis, myocyte hypertrophy, and in secondary forms, deposition of abnormal substances between myocytes. The rigid ventricles lead to elevated filling pressures and eventual heart failure.
Usage
Usage note: Must be differentiated from constrictive pericarditis, which has similar hemodynamic effects but different pathophysiology.
In Context
- "Congo red staining revealed amyloid deposits consistent with restrictive cardiomyopathy." — Pathology report
- "The patient's restrictive cardiomyopathy was secondary to cardiac sarcoidosis." — Clinical case presentation