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Professional Technical In the Industry Vocabulary Test

interrupted aortic arch

A critical congenital heart defect where there is complete discontinuity of the aortic arch.

Full Definition

Interrupted aortic arch (IAA) is a critical congenital heart defect characterized by complete anatomic discontinuity between the ascending and descending aorta. IAA is classified by the location of interruption: Type A (distal to left subclavian), Type B (between left carotid and subclavian), or Type C (between innominate and left carotid). The condition is often associated with ventricular septal defect and DiGeorge syndrome. Ductal-dependent systemic circulation requires immediate prostaglandin E1 infusion to maintain perfusion to the lower body. Surgical repair involves arch reconstruction and VSD closure, typically performed in the neonatal period.

Usage

Usage note: Specify type (A, B, or C) and associated genetic syndromes when present.

In Context

  • "The neonate with Type B interrupted aortic arch underwent single-stage complete repair." — Operative report
  • "Genetic testing revealed 22q11.2 deletion in the patient with interrupted aortic arch." — Genetics consultation

Also known as

IAA

Contrasted with

intact aortic arch

Don't confuse with

coarctation of the aorta hypoplastic left heart syndrome
inotropic support ← Back to glossary interstage period

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