Hirschsprung-associated enterocolitis
Also written as: HAEC — Hirschsprung-Associated Enterocolitis
A serious inflammatory complication of Hirschsprung disease involving the colon and small intestine.
Full Definition
Hirschsprung-associated enterocolitis (HAEC) is a potentially life-threatening inflammatory condition that occurs in patients with Hirschsprung disease, both before and after surgical correction. The condition is characterized by inflammation and distension of the colon and sometimes the small intestine, thought to result from bacterial overgrowth and altered intestinal barrier function. HAEC typically presents with fever, abdominal distension, diarrhea (often explosive and foul-smelling), and signs of systemic toxicity. The condition can lead to sepsis and death if not promptly recognized and treated. Management includes broad-spectrum antibiotics, bowel decompression, and supportive care. HAEC remains a significant cause of morbidity and mortality in Hirschsprung patients throughout their lives.
Usage
Usage note: Can use HAEC abbreviation; emphasize urgency and potential severity in documentation.
In Context
- "The patient developed HAEC requiring intensive care management and bowel decompression." — Clinical documentation
- "Recurrent episodes of Hirschsprung-associated enterocolitis prompted evaluation for incomplete resection." — Surgical consultation