Congenital Chylous Ascites
Accumulation of lymphatic fluid in the peritoneal cavity due to developmental lymphatic abnormalities. Requires specialized nutritional management.
Full Definition
Congenital chylous ascites is the accumulation of lymphatic fluid (chyle) within the peritoneal cavity due to developmental abnormalities of the lymphatic system. This condition can result from lymphatic agenesis, obstruction, or rupture of major lymphatic vessels. The ascitic fluid has a characteristic milky appearance due to its high triglyceride and lymphocyte content. Management typically involves nutritional support with medium-chain triglyceride formulas, paracentesis for symptom relief, and in some cases, surgical intervention to repair or ligate leaking lymphatic vessels. The condition may be associated with other congenital anomalies and can significantly impact respiratory function and nutritional status.
Usage
Usage note: Document triglyceride levels and appearance of ascitic fluid to support diagnosis.
In Context
- "The triglyceride level of 890 mg/dL confirmed the diagnosis of congenital chylous ascites." — Laboratory interpretation
- "Management of congenital chylous ascites included MCT formula and serial paracentesis for respiratory compromise." — Treatment plan