Congenital Lobar Emphysema
Also written as: CLE — Congenital Lobar Emphysema
Developmental lung condition with progressive overinflation of a pulmonary lobe due to bronchial obstruction or cartilage deficiency.
Full Definition
Congenital lobar emphysema is a rare developmental condition characterized by progressive overinflation of one or more pulmonary lobes due to partial bronchial obstruction or deficient bronchial cartilage support. The affected lobe becomes hyperinflated and compresses adjacent normal lung tissue and mediastinal structures. The condition typically presents in the neonatal period with progressive respiratory distress, though some cases may remain asymptomatic until later in childhood. The left upper lobe is most commonly affected, followed by the right middle lobe. Diagnosis is confirmed by imaging studies showing hyperinflation and air trapping. Treatment usually requires surgical lobectomy, which can often be performed using minimally invasive techniques.
Usage
Usage note: Document the specific lobe affected and degree of mediastinal shift in clinical notes.
In Context
- "CT imaging confirmed congenital lobar emphysema of the left upper lobe with significant mediastinal shift." — Radiology report
- "Thoracoscopic lobectomy for congenital lobar emphysema resulted in immediate improvement in respiratory mechanics." — Post-operative assessment