Dupuytren Contracture
Pronunciation: doo-pwee-TRAHNZ
Progressive fibromatosis of the palmar fascia causing finger flexion contractures, rarely seen in pediatric patients but may occur in adolescents.
Full Definition
Dupuytren contracture is a progressive fibromatosis affecting the palmar and digital fascia, leading to formation of nodules and cords that cause finger flexion contractures. While primarily an adult condition, it can rarely present in children and adolescents, often with aggressive progression and familial clustering. In pediatric cases, it may be associated with other fibromatoses or genetic syndromes. The condition typically affects the ring and little fingers first, progressing from palpable nodules to restrictive cords. Surgical intervention in pediatric patients requires careful consideration due to high recurrence rates and potential for aggressive scarring in younger patients.
Usage
Usage note: Note the French pronunciation; always capitalize Dupuytren as it's an eponym.
In Context
- "The 16-year-old presented with early Dupuytren contracture, unusual for the pediatric population." — Case presentation
- "Pediatric Dupuytren contracture often requires more aggressive treatment due to rapid progression." — Clinical guideline