Neurenteric Cyst
Pronunciation: NOOR-en-ter-ik
Rare congenital cystic lesion arising from incomplete separation of the notochord and foregut during embryonic development.
Full Definition
Neurenteric cysts are rare congenital lesions that arise from incomplete separation of the notochord and primitive foregut during early embryonic development. These cysts contain both neural and enteric elements and are lined with respiratory or gastrointestinal epithelium. They typically occur in the posterior mediastinum and may be associated with vertebral anomalies such as hemivertebrae or butterfly vertebrae. Presentations include respiratory symptoms from mass effect, recurrent infections, or spinal cord compression if there is an intraspinal component. Diagnosis is often made on MRI which shows the characteristic cystic nature and relationship to spinal structures. Complete surgical excision is the treatment of choice, though this may require multidisciplinary coordination between pediatric surgeons and neurosurgeons.
Usage
Usage note: May also be called enterogenous cyst in older literature.
In Context
- "MRI demonstrated a neurenteric cyst with intraspinal extension requiring neurosurgical consultation." — Radiology report
- "The neurenteric cyst was successfully excised through a combined thoracic and neurosurgical approach." — Operative report