bladder extrophy complex
Pronunciation: EKS-stroh-fee
Spectrum of congenital anomalies involving exposed bladder, separated pubic bones, and associated genital abnormalities.
Full Definition
Bladder exstrophy complex encompasses a spectrum of congenital malformations ranging from isolated epispadias to complete cloacal exstrophy. The classic form involves an exposed, everted bladder on the anterior abdominal wall with separated pubic symphysis and associated genital abnormalities. The condition results from failure of the cloacal membrane to be reinforced by mesenchymal tissue during embryogenesis. Management requires multidisciplinary care including staged surgical reconstruction, addressing bladder closure, epispadias repair, and later bladder neck reconstruction. Long-term outcomes focus on continence, cosmetic appearance, and sexual function.
Usage
Usage note: Specify position on the exstrophy-epispadias spectrum; note associated anomalies.
In Context
- "The neonate presented with classic bladder exstrophy complex requiring immediate multidisciplinary evaluation." — Emergency consultation note
- "Bladder exstrophy complex reconstruction was planned as a three-stage procedure beginning with primary closure." — Surgical planning conference