perineal hypospadias
Severe form of hypospadias where the urethral opening is located on the perineum rather than the glans or penile shaft.
Full Definition
The most severe form of hypospadias characterized by extreme ventral curvature of the penis and a urethral meatus located on the perineum, often near the scrotum. This condition typically presents with significant chordee, a bifid scrotum, and severe penile torsion, requiring complex multi-stage surgical reconstruction. The appearance may be ambiguous enough to prompt evaluation for disorders of sexual development. Surgical management involves chordee correction, urethral reconstruction (often requiring staged procedures), and penile straightening. The condition significantly impacts both functional and cosmetic outcomes, requiring specialized pediatric urological expertise.
Usage
Usage note: Specify degree of chordee and associated anomalies when documenting; may prompt DSD workup.
In Context
- "The newborn's perineal hypospadias required karyotype analysis to exclude intersex conditions." — Initial assessment note
- "Three-stage surgical reconstruction was planned for the complex perineal hypospadias repair." — Surgical planning note