craniosynostosis
Pronunciation: kray-nee-oh-sin-os-TOH-sis
Premature fusion of skull sutures in infants, potentially affecting brain growth and requiring surgical intervention.
Full Definition
Craniosynostosis is a condition where one or more of the sutures between the bones of an infant's skull fuse prematurely, before brain growth is complete. This premature fusion can result in abnormal head shape and potentially restrict brain growth if multiple sutures are involved. The condition may be isolated or part of a genetic syndrome. Common types include sagittal synostosis (causing a long, narrow head), coronal synostosis (causing a shortened front-to-back head dimension), and metopic synostosis (causing a triangular forehead shape). Treatment typically involves surgical correction to allow normal brain growth and improve cosmetic appearance, ideally performed within the first year of life.
Usage
Usage note: Specify the type of synostosis (sagittal, coronal, metopic, lambdoid) when known.
In Context
- "The infant was diagnosed with sagittal craniosynostosis and scheduled for surgical correction at 8 months of age." — Neurosurgery consultation note
- "Early recognition of craniosynostosis allows for optimal timing of surgical intervention." — Pediatric surgery review article