lymphatic malformation
Congenital abnormality of lymphatic vessels resulting in fluid-filled cystic lesions requiring surgical management.
Full Definition
Lymphatic malformation, previously known as lymphangioma or cystic hygroma, is a congenital developmental anomaly of the lymphatic system characterized by abnormally formed lymphatic vessels and spaces. These lesions typically present as soft, compressible, fluid-filled masses that can occur anywhere in the body but are most common in the head, neck, and axillary regions. Lymphatic malformations can be microcystic (small cysts), macrocystic (large cysts), or mixed. Treatment often requires surgical excision, though complete removal can be challenging due to the infiltrative nature of these lesions. Sclerotherapy may be used as an adjunctive treatment.
Usage
Usage note: Preferred term over older 'lymphangioma' or 'cystic hygroma' terminology.
In Context
- "The infant presented with a large cervical lymphatic malformation requiring staged surgical excision." — Pediatric surgery consultation
- "MRI revealed a macrocystic lymphatic malformation extending into the mediastinum." — Radiologic interpretation