aortic arch hypoplasia
Congenital underdevelopment of the aortic arch resulting in narrowing and potential obstruction to systemic blood flow.
Full Definition
Aortic arch hypoplasia is a congenital cardiovascular malformation characterized by underdevelopment and narrowing of the aortic arch, most commonly affecting the segment between the left carotid and left subclavian arteries (distal arch). This condition often occurs in conjunction with other congenital heart defects such as hypoplastic left heart syndrome, mitral stenosis, or ventricular septal defect. The degree of hypoplasia can range from mild narrowing to severe obstruction requiring surgical intervention. Treatment options include patch aortoplasty, end-to-end anastomosis, or more complex reconstruction depending on the extent of hypoplasia and associated lesions.
Usage
Usage note: Specify the segment of arch affected and provide Z-scores when available for pediatric patients.
In Context
- "Echocardiography revealed severe aortic arch hypoplasia with a Z-score of -3.5 requiring surgical reconstruction." — Pediatric cardiology report
- "The patient underwent arch reconstruction for hypoplasia using autologous pericardial patch augmentation." — Congenital cardiac surgery note