Aortopulmonary Window
A rare congenital heart defect characterized by an abnormal communication between the ascending aorta and main pulmonary artery above the semilunar valves.
Full Definition
Aortopulmonary window, also known as aortopulmonary septal defect, is an uncommon congenital cardiac malformation accounting for 1-3% of all congenital heart defects. The anomaly results from incomplete development of the spiral septum during embryonic heart formation, creating a communication between the ascending aorta and main pulmonary artery or right pulmonary artery. Unlike patent ductus arteriosus, which connects the descending aorta to the pulmonary artery, aortopulmonary window involves the ascending aorta and occurs above the level of the semilunar valves. The defect typically presents with early heart failure due to significant left-to-right shunting and requires prompt surgical repair to prevent development of irreversible pulmonary vascular disease.
Usage
Usage note: May be abbreviated as AP window in informal clinical discussion.
In Context
- "Echocardiography revealed a large aortopulmonary window with significant left-to-right shunting and volume overload of the left ventricle." — Echocardiography report
- "Surgical repair of the aortopulmonary window was performed using a patch closure technique with excellent postoperative results." — Operative report