Arrhythmogenic Right Ventricular Cardiomyopathy
A genetic cardiomyopathy characterized by progressive replacement of right ventricular myocardium with fibrous and adipose tissue.
Full Definition
Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is an inherited cardiac condition involving progressive replacement of right ventricular muscle with fibrous and fatty tissue, leading to ventricular arrhythmias and sudden cardiac death risk. While primarily affecting the right ventricle, left ventricular involvement may occur in advanced stages. The condition is particularly relevant in young athletes and requires careful genetic counseling and family screening. Editorial teams should note the full spelling of 'arrhythmogenic' and avoid confusion with other cardiomyopathies.
Usage
Usage note: Spell out fully on first use; ARVC acceptable as abbreviation in subsequent references.
In Context
- "Genetic testing confirmed arrhythmogenic right ventricular cardiomyopathy in the proband." — Genetics consultation report
- "The patient's family history was significant for arrhythmogenic right ventricular cardiomyopathy." — Medical history documentation