Sebaceous Gland Carcinoma
Pronunciation: seb-AY-shus gland kar-sin-OH-mah
A rare malignant tumor arising from sebaceous glands, most commonly in the periocular region. Associated with Muir-Torre syndrome and requires wide excision.
Full Definition
Sebaceous gland carcinoma is an uncommon but aggressive malignancy originating from sebaceous glands, with approximately 75% occurring in the periocular area. These tumors may arise from meibomian glands, glands of Zeis, or extraocular sebaceous glands. The malignancy is characterized by its potential for local invasion, lymphatic spread, and association with Muir-Torre syndrome in cases with concurrent visceral malignancies. Diagnosis requires careful histopathologic evaluation with oil red O staining to confirm sebaceous differentiation. Treatment involves wide local excision with careful margin assessment, and Mohs micrographic surgery is often preferred for periocular lesions to minimize tissue loss while ensuring complete removal.
Usage
Usage note: Distinguish from the more common sebaceous carcinoma terminology.
In Context
- "Periocular sebaceous gland carcinoma was confirmed with positive oil red O staining." — ophthalmologic pathology report
- "The patient required genetic counseling due to sebaceous gland carcinoma's association with Muir-Torre syndrome." — oncology consultation