pulmonary sequestration
Congenital lung malformation where abnormal lung tissue receives blood supply from systemic rather than pulmonary circulation.
Full Definition
A congenital malformation characterized by a mass of abnormal lung tissue that receives its arterial blood supply from the systemic circulation rather than the pulmonary arteries. The condition is classified as intralobar (within normal lung pleura) or extralobar (separate pleural covering). Intralobar sequestrations typically drain into pulmonary veins, while extralobar lesions may drain into systemic veins. The feeding vessel often arises from the thoracic or abdominal aorta. Prenatal diagnosis relies on identification of the characteristic systemic feeding vessel using color Doppler ultrasound. Large lesions may cause hydrops, but many remain asymptomatic and may even regress during pregnancy.
Usage
Usage note: Distinguish from CCAM by presence of systemic feeding vessel.
In Context
- "Color Doppler identified a feeding vessel from the descending aorta, confirming pulmonary sequestration." — Fetal echocardiography report
- "The extralobar pulmonary sequestration showed no signs of hydrops and remained stable throughout pregnancy." — Serial monitoring note