pseudomyxoma peritonei
Pronunciation: SOO-doh-mik-SOH-mah per-ih-ton-EE-eye
A rare condition characterized by mucinous tumor deposits throughout the peritoneal cavity, typically arising from appendiceal or ovarian tumors.
Full Definition
Pseudomyxoma peritonei is a rare clinical syndrome characterized by the accumulation of mucinous ascites and gelatinous tumor deposits throughout the peritoneal cavity. The condition most commonly arises from primary mucinous tumors of the appendix, though it can also originate from ovarian, colonic, or other intra-abdominal sources. The tumor cells produce large quantities of mucin that fills the peritoneal space, leading to progressive abdominal distension often described as 'jelly belly.' Treatment typically involves cytoreductive surgery combined with hyperthermic intraperitoneal chemotherapy (HIPEC). The condition has a unique pattern of spread, tending to redistribute to dependent portions of the abdomen while sparing certain areas like the small bowel mesentery and omentum.
Usage
Usage note: Latin term; maintain spelling exactly; often abbreviated as PMP in clinical notes.
In Context
- "The patient presented with progressive abdominal distension and imaging findings consistent with pseudomyxoma peritonei secondary to appendiceal mucinous neoplasm." — Oncology consultation note
- "Cytoreductive surgery with HIPEC was planned for the pseudomyxoma peritonei after multidisciplinary team discussion." — Surgical planning conference