Professional
Technical
IVT
radial club hand
Congenital limb deficiency involving partial or complete absence of the radius with radial deviation of the hand.
Full Definition
A congenital upper limb malformation characterized by partial or complete absence of the radius, resulting in severe radial deviation of the hand and wrist. The condition is often associated with thumb hypoplasia or aplasia, and may be part of syndromes such as VACTERL association or Holt-Oram syndrome. Treatment typically requires multiple staged surgical procedures including centralization or radialization of the wrist.
Usage
Usage note: Part of the spectrum of radial longitudinal deficiency; specify bilateral involvement when present.
In Context
- "The infant presented with bilateral radial club hand requiring staged surgical reconstruction." — Pediatric consultation note
- "Centralization was performed for severe radial club hand with excellent functional outcomes." — Surgical case report
Also known as
radial deficiency
radial longitudinal deficiency
congenital radial aplasia
Contrasted with
ulnar club hand
Don't confuse with
ulnar deficiency
Madelung deformity