craniosynostosis
Pronunciation: KRAY-nee-oh-sin-os-TOH-sis
Premature fusion of one or more cranial sutures in infants, leading to abnormal skull shape and potential brain growth restriction.
Full Definition
Craniosynostosis is a congenital or acquired condition characterized by the early closure of cranial sutures before brain growth is complete. This premature fusion prevents normal skull expansion and can lead to increased intracranial pressure, abnormal head shape, and potential developmental delays. The condition can affect single sutures (simple craniosynostosis) or multiple sutures (compound craniosynostosis). Surgical intervention typically involves cranial vault reconstruction or strip craniectomy to allow for normal brain growth and improve cosmetic appearance. The timing of surgery is crucial to optimize both functional and aesthetic outcomes.
Usage
Usage note: Specify which suture is affected (e.g., sagittal, coronal, metopic) as this determines surgical approach and prognosis.
In Context
- "The infant was diagnosed with sagittal craniosynostosis requiring early surgical correction to prevent developmental complications." — Pediatric neurosurgery consultation