truncus arteriosus
A congenital heart defect where a single large vessel arises from the heart instead of separate aorta and pulmonary artery.
Full Definition
Truncus arteriosus is a complex cyanotic congenital heart defect characterized by a single large arterial vessel arising from the heart that gives rise to the systemic, coronary, and pulmonary circulations. The defect is always associated with a large ventricular septal defect and truncal valve abnormalities. Truncus arteriosus is classified by the anatomy of the pulmonary arteries (Collett-Edwards classification). Early surgical repair, typically the Rastelli operation, is required to prevent irreversible pulmonary vascular disease. The condition accounts for approximately 1-4% of all congenital heart defects and requires staged surgical management.
Usage
Usage note: Always associated with VSD; specify type according to Collett-Edwards classification.
In Context
- "The infant with truncus arteriosus underwent complete intracardiac repair using a valved conduit." — Surgical report
- "Cardiac catheterization confirmed Type I truncus arteriosus with elevated pulmonary vascular resistance." — Catheterization report