porokeratosis
Pronunciation: por-oh-ker-ah-TOH-sis
A rare keratinization disorder characterized by a raised, ridge-like border surrounding an atrophic center.
Full Definition
Porokeratosis is a group of rare, progressive keratinization disorders that manifest as well-demarcated plaques with characteristic raised borders called cornoid lamellae. In pediatric dermatology, these lesions can appear in various forms including linear porokeratosis, which may follow Blaschko's lines. The condition requires careful documentation and monitoring as some variants carry malignant transformation risk. Early recognition is important for appropriate management and family counseling.
Usage
Usage note: Often misspelled as 'porokeratosis' with incorrect syllable emphasis. The cornoid lamella is the pathognomonic feature.
In Context
- "The linear porokeratosis extended along the patient's left arm in a Blaschko's line distribution." — dermatology consultation note
- "Biopsy confirmed porokeratosis with the characteristic cornoid lamella on histopathology." — pathology report