CCAM
Also written as: CCAM — Congenital Cystic Adenomatoid Malformation
Congenital cystic adenomatoid malformation, a developmental lung abnormality with cystic and solid components.
Full Definition
Congenital cystic adenomatoid malformation (CCAM), now more commonly called congenital pulmonary airway malformation (CPAM), is a developmental abnormality of the lung characterized by abnormal proliferation of terminal bronchioles. The lesion contains both cystic and adenomatoid (glandular) elements and is classified into five types based on cyst size and histologic features. Prenatal ultrasound may detect the lesion as an echogenic lung mass, while postnatal CT provides detailed characterization. Some lesions may regress spontaneously, while others require surgical resection due to recurrent infection or malignancy risk.
Usage
Usage note: CPAM is the preferred current terminology; specify type when known from imaging or pathology.
In Context
- "Prenatal ultrasound detected a hyperechoic lung mass suspicious for CCAM requiring postnatal imaging." — fetal ultrasound report
- "High-resolution CT confirmed Type I CCAM with large cysts in the right lower lobe." — pediatric chest CT