linear scleroderma
A form of localized scleroderma presenting as linear bands of thickened skin, often affecting limbs and potentially causing growth disturbances.
Full Definition
Linear scleroderma is a subtype of localized scleroderma characterized by linear bands or streaks of indurated, hyperpigmented skin that typically follow dermatomal patterns. In pediatric patients, this condition can be particularly problematic as it may cross joint lines and affect underlying muscle, bone, and soft tissue, potentially leading to contractures, limb length discrepancies, and functional impairment. Unlike systemic sclerosis, linear scleroderma rarely involves internal organs but requires aggressive treatment to prevent permanent deformity and growth abnormalities in developing children.
Usage
Usage note: Distinguish from 'localized scleroderma' which is the broader category encompassing linear and other subtypes.
In Context
- "The patient developed linear scleroderma extending from the shoulder to the wrist, requiring immediate immunosuppressive therapy." — Case presentation
- "Physical therapy was initiated to prevent contractures associated with the linear scleroderma lesion." — Treatment plan