subcutaneous panniculitis-like T-cell lymphoma
Also written as: SPTCL — subcutaneous panniculitis-like T-cell lymphoma
A rare form of cutaneous lymphoma that can mimic autoimmune panniculitis and present as part of hemophagocytic lymphohistiocytosis in children.
Full Definition
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is an uncommon form of primary cutaneous lymphoma that primarily affects the subcutaneous tissue, often presenting with multiple erythematous nodules and plaques. In pediatric patients, SPTCL can be associated with hemophagocytic lymphohistiocytosis and may initially be mistaken for autoimmune conditions such as lupus panniculitis or other inflammatory disorders. The diagnosis requires careful histopathological examination and immunohistochemical studies to distinguish it from reactive panniculitis. Early recognition is crucial as the condition can be aggressive and may require prompt oncologic intervention in addition to immunosuppressive therapy.
Usage
Usage note: When using the abbreviation SPTCL, always spell out the full term on first use in any document.
In Context
- "The skin biopsy revealed subcutaneous panniculitis-like T-cell lymphoma, explaining the patient's refractory panniculitis." — Pathology report
- "Hemophagocytic lymphohistiocytosis secondary to subcutaneous panniculitis-like T-cell lymphoma required immediate chemotherapy." — Oncology consultation