Bronchopulmonary Sequestration
Pronunciation: brong-koh-PUL-muh-ner-ee see-kwuh-STRAY-shuhn
Congenital lung malformation consisting of non-functioning lung tissue with abnormal arterial blood supply.
Full Definition
Bronchopulmonary sequestration is a rare congenital pulmonary malformation characterized by a mass of lung tissue that lacks normal communication with the bronchial tree and receives arterial blood supply from systemic vessels rather than pulmonary arteries. There are two types: intralobar (within normal lung tissue) and extralobar (separate from normal lung with its own pleural covering). The condition may be asymptomatic or present with recurrent infections, chest pain, or cardiac failure due to left-to-right shunting through the aberrant arterial supply.
Usage
Usage note: May be intralobar or extralobar; diagnose with CT angiography to identify feeding vessels.
In Context
- "CT angiography confirmed intralobar bronchopulmonary sequestration with feeding vessel from the descending aorta." — Radiology report
- "Lobectomy was performed for symptomatic bronchopulmonary sequestration causing recurrent pneumonia." — Thoracic surgery operative note