Congenital Microtia
Pronunciation: MY-kroh-shee-uh
Congenital underdevelopment or absence of the external ear requiring staged reconstructive surgery, often with rib cartilage grafting.
Full Definition
Congenital microtia is a birth defect characterized by underdevelopment of the external ear (auricle), ranging from mild deformity to complete absence (anotia). The condition is graded from I to IV, with Grade III being most common, involving a small, rudimentary ear structure. Surgical reconstruction typically begins around age 6-8 years when the ear has reached near-adult size and sufficient rib cartilage is available for grafting. The standard approach involves staged procedures using autologous rib cartilage to create an ear framework, followed by elevation and skin grafting. Some centers now offer prosthetic reconstruction or newer synthetic materials.
Usage
Usage note: Specify grade (I-IV) when documenting; distinguish from acquired ear deformities.
In Context
- "The patient with Grade III congenital microtia is scheduled for first-stage rib cartilage reconstruction." — Surgical scheduling note
- "Congenital microtia often presents with associated aural atresia requiring hearing evaluation." — Clinical assessment