Congenital Pulmonary Airway Malformation
Pronunciation: SEE-pam
Also written as: CPAM — Congenital Pulmonary Airway Malformation
Developmental lung anomaly with cystic or solid masses that lack normal alveolar architecture. Previously termed CCAM.
Full Definition
Congenital pulmonary airway malformation (CPAM) is a developmental anomaly of the lung characterized by abnormal proliferation of bronchial structures with formation of cysts or solid masses that lack normal alveolar development. Previously known as congenital cystic adenomatoid malformation (CCAM), the condition is classified into five types based on cyst size and histological features. Type 1 lesions have large cysts (>2cm), Type 2 have smaller cysts (<2cm), and Type 3 appears solid with microscopic cysts. These lesions can cause respiratory distress in newborns or may remain asymptomatic. Treatment typically involves surgical resection, which can often be performed thoracoscopically.
Usage
Usage note: Use current terminology (CPAM) rather than outdated CCAM in contemporary documentation.
In Context
- "Prenatal imaging revealed a Type 1 CPAM involving the right upper lobe with moderate mediastinal shift." — Fetal medicine consultation
- "Thoracoscopic resection of the CPAM was completed with preservation of normal lung parenchyma." — Operative report