Poland Syndrome
Pronunciation: POH-land
Congenital absence or underdevelopment of chest muscle and breast tissue, often with hand anomalies, requiring reconstructive surgery.
Full Definition
Poland Syndrome is a rare congenital condition characterized by underdevelopment or absence of the pectoralis major muscle on one side of the body, often accompanied by breast and nipple abnormalities. In complete forms, it may involve the pectoralis minor, serratus anterior, and external oblique muscles. Associated hand anomalies include syndactyly, brachydactyly, or absence of fingers. The condition affects the right side more commonly than the left and shows male predominance. Surgical reconstruction typically involves muscle transfer (such as latissimus dorsi flap), breast reconstruction in females, and hand surgery for digital anomalies. The timing of interventions depends on the specific defects and patient's developmental stage.
Usage
Usage note: Capitalize Poland as it's an eponym; specify complete vs. incomplete forms when documenting.
In Context
- "The adolescent with Poland syndrome underwent latissimus dorsi transfer for chest wall reconstruction." — Reconstructive surgery report
- "Poland syndrome patients require multidisciplinary care addressing both chest and hand deformities." — Treatment planning document