Univentricular Heart
A congenital cardiac malformation where only one functional ventricle is present or capable of supporting systemic circulation.
Full Definition
Univentricular heart describes a spectrum of complex congenital cardiac malformations characterized by the presence of only one functional ventricular chamber capable of supporting both systemic and pulmonary circulation. This term encompasses various anatomical variants including hypoplastic left heart syndrome, tricuspid atresia, and double inlet left ventricle. Patients typically require staged surgical palliation culminating in Fontan-type circulation. The condition presents unique physiological challenges as a single ventricle must pump blood to both systemic and pulmonary circulations. Editorial teams should maintain consistent hyphenation and distinguish from 'single ventricle' terminology.
Usage
Usage note: Hyphenate consistently; distinguish from 'single ventricle physiology' which refers to circulation patterns.
In Context
- "The neonate was diagnosed with univentricular heart requiring staged palliation." — Neonatal cardiology consultation
- "Long-term outcomes for univentricular heart depend on successful Fontan completion." — Pediatric cardiology literature review