medulloepithelioma
Pronunciation: meh-DUL-oh-ep-ih-thee-lee-OH-mah
A rare brain tumor arising from primitive medullary epithelium, primarily occurring in young children.
Full Definition
Medulloepithelioma is an extremely rare pediatric brain tumor classified as a WHO Grade IV embryonal tumor. It arises from primitive medullary epithelium and typically occurs in infants and very young children, most commonly in the cerebral hemispheres. The tumor is characterized by the formation of neural tube-like structures and may contain heterologous elements such as cartilage or striated muscle. Due to its rarity and aggressive nature, treatment protocols are not standardized and prognosis is generally poor.
Usage
Usage note: Often confused with medulloblastoma; ensure correct spelling and distinction.
In Context
- "The frontal lobe mass showed features consistent with medulloepithelioma on histopathology." — Neuropathology report
- "Given the rarity of medulloepithelioma, treatment was based on embryonal tumor protocols." — Multidisciplinary team meeting notes