Choledochal Cyst
Congenital dilatation of the bile ducts requiring surgical excision to prevent complications.
Full Definition
Choledochal cysts are congenital malformations characterized by cystic dilatation of the biliary tree, classified into five types based on location and morphology according to the Todani classification. These cysts can involve the extrahepatic bile ducts (Types I-III), intrahepatic ducts (Type IV), or both (Type V). The condition is more common in Asian populations and females, with a 4:1 female predominance. Complete surgical excision with hepaticoenterostomy is the treatment of choice to prevent complications including cholangitis, pancreatitis, and malignant transformation to cholangiocarcinoma.
Usage
Usage note: Classified using the Todani system; complete excision is preferred over drainage procedures.
In Context
- "MRI demonstrated a Type I choledochal cyst with significant bile duct dilatation." — radiology report
- "Complete excision of the choledochal cyst was performed with hepaticojejunostomy reconstruction." — operative report